Official Title
Managed Access to Investigational Use of AOC 1044 in Participants With DMD Mutations Amenable to Exon 44 Skipping
Brief Summary

The purpose of this Managed Access Program is to allow access to delpacibart zotadirsen(AOC 1044) for eligible patients diagnosed with DMD mutations amenable to exon 44skipping. The patient's Administering Physician should follow the suggested treatmentguidelines and comply with all local health authority regulations.

Detailed Description

Not Provided

Available
Treatment IND/Protocol
Muscular Disorders, Atrophic
Muscular Diseases
Musculoskeletal Diseases
Neuromuscular Diseases
Nervous System Diseases
Genetic Diseases, Inborn
Genetic Diseases, X-Linked
Muscular Dystrophies
Muscular Dystrophy, Duchenne

Drug: delpacibart zotadirsen

Del-zota is administered as an IV infusion every 6 weeks. Doses are administered based on
body weight.
Other Name: Del-zota,AOC 1044

Eligibility Criteria

Key Inclusion Criteria

Rollover Participants

- Completed Study EXPLORE44-OLE Treatment Period (through W102)

- No significant tolerability issues with AOC 1044

New (Non-Rollover) Participants

- Permanently residing in the US and have a US primary health care provider

- Documented dystrophin gene mutation that is amenable to exon 44 skipping

- Age 6 or older at the time of consent

- If previously treated with gene therapy for DMD, treatment and associated
immunosuppressive regimen was more than 12 months before consent and in the opinion
of the prescriber, participant has had an unsatisfactory treatment response

Key Exclusion Criteria

Rollover Participants

• Prescence of any new condition or worsening of existing condition that could affect
participant's safety or ability to comply with the program requirements

New (Non-Rollover) Participants

- Recently treated with or on a clinical study for another investigation drug

- Serious respiratory or cardiac dysfunction, or nearing end of life

- Screening laboratory parameters do not meet protocol requirements

- History of multiple drug allergies or to any component of AOC 1044

- Participants who discontinued early from the treatment period of EXPLORE44 or
EXPLORE44-OLE

Eligibility Gender
Male
Eligibility Age
Minimum: 6 Years ~ Maximum: N/A
Countries
United States
Locations

Arkansas Children's Hospital
Little Rock, Arkansas, United States

Rare Disease Research
Atlanta, Georgia, United States

Gillette Children's
Saint Paul, Minnesota, United States

Contacts

Clinigen Customer Service
1 877 768 4303
usmapcoordinators@clinigengroup.com

Not Provided

Clinigen Healthcare Limited
NCT Number
Keywords
Avidity
Avidity Biosciences
AOC 1044
AOC 1044-CS1
AOC 1044-CS2
EXPLORE44
EXPLORE44-OLE
Del-zota
delpacibart zotadirsen
DMD
exon skipping therapy
dystrophin
managed access
Expanded Access
Pre-approval Access
Compassionate Use
MAP
EAP
MeSH Terms
Muscular Disorders, Atrophic
Muscular Diseases
Musculoskeletal Diseases
Neuromuscular Diseases
Nervous System Diseases
Genetic Diseases, Inborn
Genetic Diseases, X-Linked
Muscular Dystrophies
Muscular Dystrophy, Duchenne