Official Title
Intermediate-Size Patient Population Expanded Access to Bezuclastinib for Patients With NonAdvanced Systemic Mastocytosis or Advanced Systemic Mastocytosis
Brief Summary

The purpose of this expanded access program (EAP) protocol is to provide investigationalbezuclastinib to patients with a diagnosis of nonadvanced systemic mastocytosis(NonAdvSM) or advanced systemic mastocytosis (AdvSM) who have received and failed or beenintolerant to at least one standard approved therapy and/or have no comparable orsatisfactory alternative therapy options.

Detailed Description

Not Provided

Available
Intermediate-size Population
Systemic Mastocytoses, Indolent
Systemic Mastocytoses, Aggressive

Drug: Bezuclastinib

Drug: Bezuclastinib Tablets
Other Name: CGT9486

Eligibility Criteria

Key Inclusion Criteria:

- Able to provide written informed consent and commit to EAP assessments.

- ≥18 years of age.

- Able to swallow tablets.

- Diagnosed with ASM, SM-AHN, MCL, BMM, ISM, or SSM according to the 2022 WHO
Classification for SM

- Not receiving adequate disease control on current therapy(ies).

- Have clinically acceptable laboratory screening results.

Exclusion Criteria:

- Patients who are eligible for and/or enrolled in an on-going bezuclastinib clinical
trial.

- Patients who discontinued investigational use of bezuclastinib in previous clinical
trials due to toxicity or withdrawal of consent.

- Pregnant or currently breastfeeding.

- Prior or ongoing clinically significant illness or medical or physical condition

Other protocol-defined criteria apply.

Eligibility Gender
All
Eligibility Age
Minimum: 18 Years ~ Maximum: N/A
Countries
United States
Locations

Orso Health/Modena Asthma Allergy
La Jolla, California, United States

Scripps Green Hospital
La Jolla, California, United States

UCLA Ronald Reagan Medical Center
Los Angeles, California, United States

Sneeze Wheeze & Itch Associates LLC Clinical Research Center
Normal, Illinois, United States

Indiana University Health
Indianapolis, Indiana, United States

Walter Reed
Bethesda, Maryland, United States

AllerVie Health
Glenn Dale, Maryland, United States

Boston Specialists
Boston, Massachusetts, United States

Dana Farber Cancer Institute
Boston, Massachusetts, United States

Michigan Medicine- University of Michigan
Ann Arbor, Michigan, United States

Mayo Clinic
Rochester, Minnesota, United States

Dartmouth-Hitchcock Medical Center
Lebanon, New Hampshire, United States

Memorial Sloan Kettering Cancer Center
New York, New York, United States

Duke Blood Cancer Center
Durham, North Carolina, United States

The Ohio State University Wexner Medical Center
Columbus, Ohio, United States

AIR Care
Dallas, Texas, United States

Texas Children's Hospital
Houston, Texas, United States

The University of Texas, MD Anderson Cancer Center
Houston, Texas, United States

Contacts

Alexandra Malinowski, PharmD
1-877-633-8049
EAP@cogentbio.com

Rachael Easton, MD, PhD, Study Director
Cogent Biosciences, Inc.

Cogent Biosciences, Inc.
NCT Number
Keywords
Systemic Mastocytosis
NonAdvanced Systemic Mastocytosis
Advanced Systemic Mastocytosis
Systemic Mastocytosis with an associated hematologic neoplasm (SM-AHN)
Aggressive Systemic Mastocytosis (ASM)
Mast Cell Leukemia (MCL)
Bone Marrow Mastocytosis (BMM)
MeSH Terms
Mastocytosis, Systemic
Leukemia, Mast-Cell